A Case of Primary Rhabdomyosarcoma in the Left Cerebello-Pontine Angle.

Shim, Sung Bo; Jun, Yong Moon; Ok, Yung Chul; Lee, Kyu Woong; Kim, Jeong Rae; Park, Moon Hyang

Original Article

Journal of Korean Neurosurgical Society 1977;6(1): 215-220.

Sung Bo Shim, Yong Moon Jun, Yung Chul Ok, Kyu Woong Lee, Jeong Rae Kim, Moon Hyang Park

¹Department of Neurosurgery, National Medical Center, Korea.
²Department of Pathology, National Medical Center, Korea.

ABSTRACT

The primary rhabdomyosarcoma of the brain is very rare. There are only 14 cases reported in the literatures till 1975, and the majority of them were arised in the cerebellum. The intracranial rhabdomyosarcomas may be originated from the multipotent mesenchymal cells of aberrent muscle tissue in the leptomeninges. The histological 3 types are adult pleomorphic, alveolar and embryonal type. The demonstration of cross-striation is confirmed for diagnosis of this tumor. All of these tumors tend to have a short clinical course, but the survival time seems to be slightly improved by surgical excision followed by radiotherapy. We have recently experienced one case of primary rhabdomyosarcoma in the left cerebellopontine angle of 9 year-old girl, which was confirmed by operation and complete autopsy.