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Journal of Korean Neurosurgical Society 2002;32(6): 599-602. |
Atypical Teratoid/Rhabdoid Tumor in Central Nervous System: Report of 2 Cases. |
Jae Myung Kim, Young Shin Ra, Thad T Ghim, Shin Kwang Khang |
1Department of Neurological Surgery, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea. ysra@amc.seoul.kr 2Department of Pediatrics, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea. 3Department of Pathology, Asan Medical Center, College of Medicine, University of Ulsan, Seoul, Korea. |
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ABSTRACT |
We report two cases of atypical teratoid/rhabdoid tumor(AT/RT) in the central nervous system. Primary central nervous system AT/RT is an extremely rare malignant tumor affecting infants and young children. These tumors have been diagnosed previously as primitive neuroectodermal tumors(PNETs) because AT/RT contains fields indistinguishable from classic PNETs. Separation of these two tumor types is crucial because the prognosis for AT/RT is poor even when treatment includes surgery with or without radiation therapy and/or chemotherapy. Clinical, radiological and histopathological features of AT/RT are presented. |
Key Words:
Atypical teratoid/rhabdoid tumor; Surgery; Child; Chemotherapy |
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